Carnitine O-palmitoyltransferase explained

Symbol:	Carn_acyltransf
Choline/Carnitine o-acyltransferase
Pfam:	PF00755
Pfam Clan:	CL0149
Interpro:	IPR000542
Prosite:	PDOC00402
Scop:	1ndi
Opm Family:	83
Opm Protein:	2h3u

Carnitine O-palmitoyltransferase (also called carnitine palmitoyltransferase) is a mitochondrial transferase enzyme involved in the metabolism of palmitoylcarnitine into palmitoyl-CoA. A related transferase is carnitine acyltransferase.

Human forms

There are four different forms of CPT in humans:

• CPT1A – associated with Carnitine palmitoyltransferase I deficiency
• CPT1B
• CPT1C
• CPT2 – associated with carnitine palmitoyltransferase II deficiency

External links

• – Acyltransferases ChoActase / COT / CPT family in PROSITE
• Choline/Carnitine o-acyltransferase family in Pfam