TMEM38A explained

Trimeric intracellular cation-selective channel A (TRIC-A) is a monovalent cation channel in the SR and nuclear membranes of skeletal muscle cells,[1] [2] encoded by the transmembrane protein 38A (TMEM38A) gene. It is one of two known TRIC proteins, the other being TRIC-B.

Structure

TRIC-A is a 33kDa[3] transmembrane protein, expressed predominantly in excitable tissues including skeletal muscle and brain. Its N-terminal region is located in the SR lumen or within the nucleus while its C-terminal region projects into the cytoplasm. In situ, TRIC-A forms homo-trimers, producing its "bullet-shaped" three-dimensional structure (see Venturi et al. (2012), Figure 1 for a three-dimensional rendering of TRIC-A).

Function

TRIC-A is permeable to both Na+ and K+ but not divalent cations like Ca2+. The channel exhibits marked voltage-dependence, becoming more open when the cytosol is more positively charged than the ER lumen. TMEM38A-knockout mice exhibit reduced Ryanodine receptor 1-mediated Ca2+ release; as such, K+ flux into the SR through TRIC-A is thought to support RyR1-mediated efflux of Ca2+ ions from the sarcoplasmic reticulum into the cytosol. These knockouts also develop hypertension during early adulthood, whereas transgenic mice overexpressing TRIC-A develop hypotension. These results are thought to reflect a role for TRIC-A in the excitability of vascular smooth muscle cells.

Clinical significance

TRIC-A has been implicated in the regulation of arterial blood pressure through regulating the excitability of vascular smooth muscle cells. Several single-nucleotide polymorphisms (SNPs) in close proximity to the TRIC-A locus increase the risk of hypertension and reduce the efficiency of antihypertensive drugs in its treatment.[4] Such SNPs are in positive linkage disequilibrium with TRIC-A, meaning they are unlikely to be separated by genetic recombination and so are more frequently inherited together from the same parent chromosome. As such, TRIC-A SNPs can provide biomarkers for the diagnosis of essential hypertension and, in future, may help to determine which treatments may be most well-suited to a given individual (see personalized medicine).

See also

Notes and References

  1. Elisa. Venturi. Rebecca . Sitsapesan . Rebecca Sitsapesan . Daiju . Yamazaki . Hiroshi . Takeshima . TRIC channels supporting efficient Ca2+ release from intracellular stores . European Journal of Physiology. 465. 187–195 . 15 December 2012. 2. 10.1007/s00424-012-1197-5. 23242030. 14397400.
  2. Wayne A. . Cabral . Masaki . Ishikawa. Matthias . Garten. Elena N. . Makareeva. Brandi M. . Sargent. MaryAnn . Weis. Aileen M. . Barnes. Emma A. . Webb. Nicholas J. . Shaw. Leena . Ala-Kokko. Felicitas L. . Lacbawan. Wolfgang . Högler. Sergey . Leikin. Paul S. . Blank. Joshua . Zimmerberg. David R. . Eyre. Yoshihiko . Yamada. Joan C. . Marini . Absence of the ER Cation Channel TMEM38B/TRIC-B Disrupts Intracellular Calcium Homeostasis and Dysregulates Collagen Synthesis in Recessive Osteogenesis Imperfecta . 10.1371/journal.pgen.1006156 . 21 July 2016 . PLOS Genetics . 12 . 7. e1006156 . 27441836 . 4956114 . free .
  3. TRIC channels are essential for Ca2+ handling in intracellular stores . 5 July 2007. Nature . 448 . 78–82 . 10.1038/nature05928 . Masayuki . Yazawa. Christopher. Ferrante. Jue . Feng. Kazuhiro . Mio. Toshihiko . Ogura. Miao . Zhang. Pei-Hui . Lin. Zui . Pan. Shinji . Komazaki. Kazuhiro . Kato. Miyuki . Nishi. Xiaoli . Zhao. Noah . Weisleder. Chikara . Sato. Jianjie . Ma . Hiroshi . Takeshima. 7149 . 17611541 . 2007Natur.448...78Y . 4431703 .
  4. TRIC-A Channels in Vascular Smooth Muscle Contribute to Blood Pressure Maintenance . 10.1016/j.cmet.2011.05.011 . 14 . 2 . 3 August 2011 . Cell Metabolism . 231–241 . Daiju . Yamazaki. Yasuharu . Tabara. Satomi . Kita. Hironori . Hanada. Shinji . Komazaki. Daisuke . Naitou. Aya . Mishima. Miyuki . Nishi. Hisao . Yamamura. Shinichiro . Yamamoto. Sho . Kakizawa. Hitoshi . Miyachi. Shintaro . Yamamoto. Toshiyuki . Miyata. Yuhei . Kawano. Kei . Kamide. Toshio . Ogihara. Akira . Hata. Satoshi . Umemura. Masayoshi . Soma. Norio . Takahashi. Yuji . Imaizumi. Tetsuro . Miki. Takahiro . Iwamoto. Hiroshi . Takeshima. 21803293 . 2433/143634 . free .