| Senter syndrome | |
| Synonyms: | Desmons' syndrome[1] |
| Field: | Dermatology |
Senter syndrome is a cutaneous condition characterized by similar skin changes and congenital hearing impairment to keratitis–ichthyosis–deafness syndrome, but is associated with glycogen storage leading to hepatomegaly, hepatic cirrhosis, growth failure and intellectual disability.[2]