Pigmented purpuric dermatosis explained

Pigmented purpuric dermatosis
Synonyms:	Progressive pigmentary dermatosis, Purpura pigmentosa chronica, Pigmentary purpuric eruptions, or Progressive pigmenting purpura or Schamberg's disease

Pigmented purpuric dermatosis refers to one of the three major classes of skin conditions characterized by purpuric skin eruptions.

Pigmented purpuric dermatosis are distinguished from other purpura by size (0.3–1 cm) and are most often seen in the lower extremities.^[1] Pigmentary purpuric eruptions may present with one of several clinical patterns. There may be overlapping characteristics among pigmented purpuric dermatosis and between their signs and those of other purpuric eruptions. Examples of the pigmented purpuric dermatosis group include:

• Schamberg's disease

• Majocchi's disease (Purpura annularis telangiectodes)

• Gougerot-Blum syndrome (Pigmented purpuric lichenoid dermatitis)

• Ducas and Kapetanakis pigmented purpura

• Lichen aureus

Although vascular damage may be present, it is insufficient for these conditions to be considered forms of vasculitis.^[2]

A few very small non-blinded studies of treatment with narrow-band ultraviolet light have been reported as promising.^[3]

See also

• Purpura
• Skin lesion
• List of cutaneous conditions

Notes and References

1. Book: James, William D. . Berger, Timothy G. . Andrews' Diseases of the Skin: clinical Dermatology . Saunders Elsevier . 2006 . 978-0-7216-2921-6 . etal.
2. Book: David E. Elder. Rosalie Elenitsas. Michael D Ioffreda. Bernett L. Johnson, Jr.. Atlas and synopsis of Lever's histopathology of the skin. 22 May 2010. 2007. Lippincott Williams & Wilkins. 978-0-7817-6845-0. 127–.
3. Summarized in 2015 by Tapan Kumar Dhali, Monica Chahar, and Mohammad Asad Haroon in

   Phototherapy as an effective treatment for Majocchi's disease - Case report

   An Bras Dermatol. 2015 Jan-Feb; 90(1): 96–99.