Many conditions of or affecting the human integumentary system have associated abnormalities of the teeth.
| Abnormality | Condition(s) | |
|---|---|---|
| Hypohidrotic ectodermal dysplasia Incontinentia pigmenti Congenital syphilis | ||
| Herlitz variant of junctional epidermolysis bullosa Tuberous sclerosis Gorlin syndrome Tricho–dento–osseous syndrome | ||
| Hyper-IgE syndrome | ||
| Gardner syndrome | ||
| Gardner syndrome | ||
| Hypomelanosis of Ito Schöpf–Schulz–Passarge syndrome Hypohidrotic ectodermal dysplasia EEC syndrome AEC syndrome | ||
| Congenital erythropoietic porphyria Hepatoerythropoietic porphyria | ||
| Bulimia | ||
| Loss of deciduous and permanent teeth by late childhood | Papillon–Lefèvre syndrome Haim–Munk syndrome | |
| Premature dentition (Natal teeth) | Pachyonychia congenita type II | |
| Grey–green discoloration of the mid-portion of permanent teeth | Minocycline-induced pigmentation | |
| Brown discoloration of gingival third of teeth | Tetracycline-induced pigmentation |