Congenital self-healing reticulohistiocytosis explained
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Synonyms: | Hashimoto–Pritzker disease,[1] and Hashimoto–Pritzker syndrome |
Field: | dermatology |
Congenital self-healing reticulohistiocytosis is a condition that is a self-limited form of Langerhans cell histiocytosis.[2]
Symptoms
Non-specific inflammatory response, which includes fever, lethargy, and weight loss. This is suspected of being a genetic disorder, and as the name implies, is self healing.
- Skin: Commonly seen are a rash which varies from scaly erythematous lesions to red papules pronounced in intertriginous areas. Up to 80% of patients have extensive eruptions on the scalp.
- Lymph node: Enlargement of the lymph nodes in 50% of Histiocytosis cases.[3]
History
It was first described by Ken Hashimoto and M. S. Pritzkar in 1973.[4] [5]
See also
Notes and References
- Book: Rapini, Ronald P. . Bolognia, Jean L. . Jorizzo, Joseph L. . Dermatology: 2-Volume Set . Mosby . St. Louis . 2007 . 978-1-4160-2999-1 .
- Book: James, William D. . Berger, Timothy G. . Andrews' Diseases of the Skin: clinical Dermatology . Saunders Elsevier . 2006 . 978-0-7216-2921-6 . etal.
- Web site: Langerhans Cell Histiocytosis - Patient UK . 2007-05-10 . 2012-02-12 . https://web.archive.org/web/20120212150828/http://www.patient.co.uk/showdoc/40002781/#notes . dead .
- Book: John Thorne Crissey. Lawrence C. Parish. Karl Holubar. Historical Atlas of Dermatology and Dermatologists. 2013. CRC Press. 978-1-84214-100-7. 179.
- Lee. Young H.. Talekar. Mala K.. Chung. Catherine G.. Bell. Moshe D.. Zaenglein. Andrea L.. February 2014. Congenital Self-Healing Reticulohistiocytosis. The Journal of Clinical and Aesthetic Dermatology. 7. 2. 49–53. 1941-2789. 3935651. 24578781.