Harrington–Hollingsworth experiment explained

The Harrington–Hollingsworth experiment was an experiment that established the autoimmune nature of the blood disorder immune thrombocytopenic purpura.[1] [2] It was performed in 1950 by the academic staff of Barnes-Jewish Hospital in St. Louis, Missouri.[2] __TOC__

Experiment

The experiment was undertaken in 1950 by William J. Harrington and James W. Hollingsworth, who postulated that in patients with idiopathic thrombocytopenic purpura (ITP), it was a blood factor that caused the destruction of platelets.[2] To test this hypothesis, Harrington received 500 ml of blood from a patient with ITP.[2] Within three hours, his platelets dropped to dangerously low levels and he experienced a seizure.[2] His platelet count remained extremely low for four days, finally returning to normal levels by the fifth day.[2] Bone marrow biopsy from Harrington's sternum demonstrated normal megakaryocytes, the cells necessary for platelet production.[2]

Subsequently the experiment was repeated on all suitable staff members at the Barnes-Jewish Hospital. All subjects developed low platelet counts within three hours, and all recovered after a period of several days.[2]

Implications

Schwartz notes that the Harrington–Hollingsworth experiment was a turning point in the understanding of ITP's pathophysiology:

The experiment was the first to demonstrate that infusion of an ITP patient's plasma into a normal patient caused a precipitous drop in platelet count.[2] This suggested that low platelet counts (thrombocytopenia) in patients with ITP was caused by a circulating factor found in the blood.[2] Many studies performed since then have demonstrated that this circulating factor is in fact a collection of immunoglobulins.[3] [4] Many physician-scientists believe the findings had a major influence on the field of autoimmunity, which was not universally accepted at the time as a mechanism of human disease.

Notes and References

  1. Harrington WJ, Minnich V, Hollingsworth JW, Moore CV . Demonstration of a thrombocytopenic factor in the blood of patients with thrombocytopenic purpura . J. Lab. Clin. Med. . 38 . 1 . 1–10 . July 1951 . 14850832 .
  2. Schwartz RS . Immune thrombocytopenic purpura--from agony to agonist . N. Engl. J. Med. . 357 . 22 . 2299–301 . 2007 . 18046034 . 10.1056/NEJMe0707126.
  3. Tomer A, Koziol J, McMillan R . Autoimmune thrombocytopenia: flow cytometric determination of platelet-associated autoantibodies against platelet-specific receptors . J. Thromb. Haemost. . 3 . 1 . 74–8 . January 2005 . 15634268 . 10.1111/j.1538-7836.2004.01052.x. free .
  4. Li J, Yang C, Xia Y, etal . Thrombocytopenia caused by the development of antibodies to thrombopoietin . Blood . 98 . 12 . 3241–8 . December 2001 . 11719360 . 10.1182/blood.V98.12.3241. free .