Erythromelanosis follicularis faciei et colli explained

Specialty:	Dermatology

Erythromelanosis follicularis faciei et colli is an erythematous pigmentary disease involving the follicles, characterized by a reddish-brown, sharply demarcated, symmetrical discoloration involving the preauricular and maxillary regions.^[1]

Signs and symptoms

Erythromelanosis follicularis faciei et colli is characterized by patches of erythema (with or without telangiectasia), follicular papules (follicular plugging), and bilateral and symmetrical hyperpigmentation (reddish-brown pigmentation) that start on the preauricular areas and cheeks and can eventually migrate to the submandibular portions of the neck.^[2]

Causes

Although the cause of this disorder is unknown, familial cases, spontaneous mutation, and an autosomal recessive pattern of inheritance have all been documented.^{[3] [4]}

Diagnosis

Histopathologic observations include vascular dilatation in the upper dermis, hyperkeratosis, follicular plugging, and enhanced basal membrane pigmentation.^[5]

Treatment

Topical therapies include metronidazole, ammonium lactate, tacalcitol ointment, retinoids, hydroquinone, and salicylic acid.^[5] There have been reports of erythema and hyperpigmentation treated with pulsed dye laser or .^[6]

See also

• Pigmentatio reticularis faciei et colli
• List of cutaneous conditions

Further reading

• Al‐Saif . Fahad Mohammad . Baqays . Abdullah Ali . AlSaif . Hadeel Fahad . Alhumidi . Ahmed Abdullah . Erythromelanosis follicularis faciei et colli with reticulated hyperpigmentation of the extremities . Clinical Case Reports . Wiley . 5 . 10 . 2017-08-16 . 2050-0904 . 10.1002/ccr3.1095 . 1576–1579 . none. 5628235 .
• Errichetti . E. . Pizzolitto . S. . Stinco . G. . Dermoscopy of Erythromelanosis Follicularis Faciei et Colli . Actas Dermo-Sifiliográficas (English Edition) . Elsevier BV . 108 . 8 . 2017 . 1578-2190 . 10.1016/j.adengl.2017.04.010 . 779–781 . none. free .

External links

• VisualDx

Notes and References

1. James, William; Berger, Timothy; Elston, Dirk (2005). Andrews' Diseases of the Skin: Clinical Dermatology. (10th ed.). Saunders. .
2. Rather . Shagufta . Yaseen . Atiya . Mukhija . Mani . Erythromelanosis follicularis faciei et colli - A cross-sectional, descriptive study . Indian Journal of Dermatology . Medknow . 61 . 3 . 2016 . 0019-5154 . 10.4103/0019-5154.182419 . free . 308. 4885184 .
3. YANEZ . S. . VELASCO . J. A. . GONZALEZ . M. P. . Familial erythromelanosis follicularis faciei et colli-an autosomal recessive mode of inheritance . Clinical and Experimental Dermatology . Oxford University Press (OUP) . 18 . 3 . 1993 . 0307-6938 . 10.1111/j.1365-2230.1993.tb02190.x . 283–285.
4. Augustine . M . Jayaseelan . E . Erythromelanosis follicularis faciei <i>et</i> colli: Relationship with keratosis pilaris . Indian Journal of Dermatology, Venereology and Leprology . Scientific Scholar . 74 . 1 . 2008 . 0378-6323 . 10.4103/0378-6323.38409 . free . 47.
5. Thielmann . Carl Maximilian . Sondermann . Wiebke . Erythromelanosis Follicularis Faciei et Colli: A Case Report in a Caucasian Male and Brief Review of the Literature . Case Reports in Dermatology . 12 . 3 . 2020-11-16 . 1662-6567 . 33362509 . 7747045 . 10.1159/000511370 . 231–235.
6. Al Hawsawi . Khalid . Aljuhani . Ohood . Niaz . Ghassan . Fallatah . Haneen . Alhawsawi . Abrar . Erythromelanosis Follicularis Faciei: A Case Report and Review of the Literature . Case Reports in Dermatology . 7 . 3 . 2015-11-27 . 1662-6567 . 26955328 . 4777903 . 10.1159/000442343 . 335–339.