The Chapel Hill Consensus Conferences (CHCC) (1994 and 2012) are a pair of international conferences which addressed the need of standardized classification system for systemic vasculitides.[1] [2]
| Classification Group | Diseases | |
|---|---|---|
| Large-vessel vasculitis (LVV) | Takayasu's arteritis (TAK); Giant-cell arteritis (GCA) | |
| Medium-vessel vasculitis (MVV) | Polyarteritis nodosa (PAN), Kawasaki disease (KD) | |
| Small vessel vasculitis (SVV) | ANCA-associated vasculitis (AAV); Immune complex SVV | |
| Variable vessel vasculitis (VVV) | Behcet's disease (BD); Cogan's syndrome (CS) | |
| Single Organ Vasculitis (SOV) | Cutaneous leukocytoclastic angiitis; cutaneous arteritis; primary central nervous system vasculitis; isolated aortitis; others | |
| Vasculitis associated with systemic disease | Lupus vasculitis; Rheumatoid vasculitis; Sarcoid vasculitis; others | |
| Vasculitis associated with probable etiology | Hepatitis C virus-associated cryoglobulinemic vasculitis; Hepatitis B virus-associated vasculitis; Syphilis-associated aortitis; Drug-associated immune complex vasculitis; Cancer-associated vasculitis; others |