Acute idiopathic blind spot enlargement syndrome explained

Acute idiopathic blind spot enlargement syndrome
Synonyms:AIBSE syndrome
Field:Ophthalmology
Diagnosis:Eye examination, Visual field test
Treatment:Nil, Usually self limiting

Acute idiopathic blind spot enlargement syndrome (AIBSE) is a rare eye disease affecting the retina of the eye. It is basically a type of retinopathy which affects females more than males. Currently there is no treatment for this condition, but, it is usually self limiting.

Cause

Though exact etiology of AIBSE syndrome is unknown, studies shows that viral illness like influenza and vaccinations like MMR may trigger the condition.[1]

Demographics

AIBSE syndrome affects females more than males.[1] Higher incidence is seen in Caucasian people.[1]

Signs and Symptoms

Enlargement of blind spot area in the visual field of the eye is the main sign and acute onset photopsia is the main symptom of AIBSE syndrome.[2] Other symptoms include monocular scotoma and reduced light perception.[3]

Diagnosis

Diagnostic techniques like ophthalmoscopy, visual field test, optical coherence tomography, fluorescein angiography, multifocal electroretinography and electrophysiology may be used in diagnosing AIBSE syndrome.[2] Subjective measurement of blind spot enlargement is done using visual field testing.[4] In the early stages, using FFA peripapillary hyperfluorescence may be observed.[4] Since OCT can be used to observe the microstructural alterations in the outer retina, it is the gold standard in diagnosing AIBSES.[2]

Treatment

Currently there is no treatment for this condition, but, it is usually self limiting.[1] Systemic administration of corticosteroids may be advised.[2] Even if the disease is resolved, the enlarged blind spot usually does not return to normal.[5]

History

Fletcher et al. first described AIBSE syndrome in 1988.[2]

Notes and References

  1. Web site: Acute Idiopathic Blind Spot Enlargement (AIBSE) Syndrome - EyeWiki . eyewiki.aao.org.
  2. Zimmermann . Julian A. . Eter . Nicole . Biermann . Julia . Acute Idiopathic Blind Spot Enlargement Syndrome—New Perspectives in the OCT Era . Journal of Clinical Medicine . 7 September 2022 . 11 . 18 . 5278 . 10.3390/jcm11185278 . free . 36142923 . 9501978 . 2077-0383.
  3. Wong . Melody . Campos-Baniak . Maria Gabriela . Colleaux . Kevin . Acute idiopathic blind spot enlargement syndrome following measles, mumps and rubella vaccination . Canadian Journal of Ophthalmology . August 2019 . 54 . 4 . e199–e203 . 10.1016/j.jcjo.2018.09.005 . 31358170 .
  4. Ishihara . Rhys . Khan . Youan . Halim . Muhammad Sohail . Akhavanrezayat . Amir . Onghanseng . Neil . Levin . Marc Harris . Nguyen . Quan Dong . Acute idiopathic blind spot enlargement syndrome (AIBSES) with retinal vasculitis . American Journal of Ophthalmology Case Reports . March 2023 . 29 . 101760 . 10.1016/j.ajoc.2022.101760 . 36561880 . 9763352 . 2451-9936.
  5. Web site: The Case of the Enormous Blind Spot . Retina Today . en.