ADAM20 explained

Disintegrin and metalloproteinase domain-containing protein 20 is an enzyme that in humans is encoded by the ADAM20 gene. It is a membrane disintegrin-metalloprotease that belongs to the ADAM family. It is exclusively expressed in Testes and is similar to sperm cell-specific fertilins -alpha and -beta.

Its cDNA is tightly linked to marker SHGC-36001 on chromosome 14q24.1. ADAM20 is related to fertilin α (ADAM1A/B pseudogene), fertilin β (ADAM2), and fertilin γ (ADAM9). In humans, fertilin α has recently been deactivated so ADAM20 may be the functional equivalent fertilin α in humans.[1]

Structure

In common with other ADAM family members, ADAM20 contains a N-terminal reprolysin family propeptide (residues 57–159), reprolysin (M12B) family zinc metalloprotease domain (207–395), disintegrin domain (416–488), and a C-terminal ADAM cysteine-rich domain (493–605).[2]

The propeptide acts both a signal peptide and an activator domain. This prodomain has a cysteine that interacts with a zinc in the catalytic domain, thereby preventing the catalytic activity of the protein.When the pro-protein domain is cleaved, this cysteine zinc bond is broken and the protein is activated.[3] A notable variant showed an amino acid difference in the pro protein domain that prevented the cleavage of this domain which prevented the fusion of the sperm cell to an egg.[4]

Notes and References

  1. Hooft van Huijsduijnen R . ADAM 20 and 21; two novel human testis-specific membrane metalloproteases with similarity to fertilin-alpha . Gene . 206 . 2 . 273–82 . January 1998 . 9469942 . 10.1016/s0378-1119(97)00597-0 .
  2. Web site: Disintegrin and metalloproteinase domain-containing protein 20 . Pfam . InterPro .
  3. Van Wart HE, Birkedal-Hansen H . The cysteine switch: a principle of regulation of metalloproteinase activity with potential applicability to the entire matrix metalloproteinase gene family . Proceedings of the National Academy of Sciences of the United States of America . 87 . 14 . 5578–82 . July 1990 . 2164689 . 54368 . 10.1073/pnas.87.14.5578 . 1990PNAS...87.5578V . free .
  4. Sha YW, Xu X, Ji ZY, Mei LB, Qiu PP, Ji H, Li P, Li L, Liu WW . Sperm-egg fusion disorder in a Chinese male patient was associated with a rare ADAM20 variant . Oncotarget . 9 . 2 . 2086–2091 . January 2018 . 29416755 . 5788623 . 10.18632/oncotarget.23331 .